{"id":75775,"date":"2026-03-11T15:32:00","date_gmt":"2026-03-11T15:32:00","guid":{"rendered":"https:\/\/www.africa-press.net\/senegal\/politique\/celine-dion-et-le-syndrome-de-la-personne-raide"},"modified":"2026-04-19T21:01:29","modified_gmt":"2026-04-19T21:01:29","slug":"celine-dion-et-le-syndrome-de-la-personne-raide","status":"publish","type":"post","link":"https:\/\/www.africa-press.net\/senegal\/toutes-les-actualites\/celine-dion-et-le-syndrome-de-la-personne-raide","title":{"rendered":"C\u00e9line Dion et le syndrome de la personne raide"},"content":{"rendered":"<p><span class=\"ap-article-header-tag\"> <strong>Africa-Press &#8211; Senegal. <\/strong> <\/span>Depuis 2022, la chanteuse canadienne avait quasiment abandonne\u0301 la sce\u0300ne, a\u0300 l\u2019exception d\u2019une apparition lors de la ce\u0301re\u0301monie d\u2019ouverture des Jeux olympiques de Paris 2024. En cause, une maladie neurologique rare: le syndrome de la personne raide, e\u0301galement dit de Moersch-Woltman.<\/p>\n<p>La situation de la star internationale a attire\u0301 l\u2019attention sur cette pathologie jusqu\u2019alors inconnue du grand public. Les estimations les plus courantes e\u0301voquent un cas sur un million de personnes. Certains spe\u0301cialistes de la maladie, comme la neurologue ame\u0301ricaine Amanda Piquet qui soigne la chanteuse, estiment pluto\u0302t sa fre\u0301quence a\u0300 un ou deux cas sur 100.000, en raison d\u2019un probable sous-diagnostic.<\/p>\n<p>\u00ab On n\u2019a pas de donne\u0301es statistiques fiables \u00bb<\/p>\n<p>\u00ab On n\u2019a pas de donne\u0301es statistiques fiables: dans ces maladies ultra-rares, on est toujours sur des estimations assez grossie\u0300res \u00bb, admet aupre\u0300s de l\u2019AFP Pierre-Franc\u0327ois Pradat, neurologue a\u0300 l\u2019ho\u0302pital parisien de la Pitie\u0301-Salpe\u0302trie\u0300re (AP-HP).<\/p>\n<p>En tout e\u0301tat de cause, ce syndrome, qui touche principalement des femmes, reste une maladie rare qui met souvent des anne\u0301es a\u0300 e\u0302tre diagnostique\u0301e. Ses sympto\u0302mes ressemblent a\u0300 des pathologies plus fre\u0301quentes comme la scle\u0301rose en plaque, ce qui complique son identification. \u00ab Comme c\u2019est douloureux, c\u0327a peut e\u0302tre aussi confondu avec des proble\u0300mes rhumatologiques \u00bb, ajoute M. Pradat.<\/p>\n<p>Image tire\u0301e d\u2019une vide\u0301o diffuse\u0301e par le Service de radiodiffusion olympique montrant la chanteuse canadienne Ce\u0301line Dion se produisant sur la tour Eiffel lors de la ce\u0301re\u0301monie d\u2019ouverture des Jeux olympiques de Paris 2024, le 26 juillet 2024 a\u0300 Paris (POOL\/AFP\/Archives \u2013 -)<\/p>\n<p>La maladie se caracte\u0301rise par une raideur musculaire progressive et des e\u0301pisodes re\u0301pe\u0301te\u0301s de spasmes musculaires douloureux. Ces derniers peuvent survenir au hasard ou e\u0302tre de\u0301clenche\u0301s par une varie\u0301te\u0301 d\u2019e\u0301ve\u0301nements diffe\u0301rents, y compris un bruit soudain ou un le\u0301ger contact physique.<\/p>\n<p>\u00ab C\u2019est comme si quelqu\u2019un vous e\u0301tranglait \u00bb, avait te\u0301moigne\u0301 Ce\u0301line Dion en juin 2024, pre\u0301cisant que la douleur pouvait traverser tout son corps et que les spasmes lui ont parfois casse\u0301 les co\u0302tes. Un passage d\u2019un documentaire diffuse\u0301 peu apre\u0300s montrait la star en pleine crise, comple\u0300tement immobile et incapable de parler.<\/p>\n<p>Un de\u0301re\u0300glement du syste\u0300me immunitaire?<\/p>\n<p>\u00ab L\u2019a\u0302ge d\u2019apparition est d\u2019environ 45 ans et les sympto\u0302mes se de\u0301veloppent sur plusieurs mois ou anne\u0301es \u00bb, explique Orphanet, un portail francophone sur les maladies rares, soulignant que le pronostic est \u00ab tre\u0300s variable \u00bb.<\/p>\n<p>La cause n\u2019est pas connue avec certitude, mais la piste la plus probable est un de\u0301re\u0300glement du syste\u0300me immunitaire. Chez la plupart des patients, on trouve un taux anormalement e\u0301leve\u0301 de certains anticorps, ce qui appuie cette hypothe\u0300se.<\/p>\n<p>La chanteuse canadienne Ce\u0301line Dion apparai\u0302t sur un e\u0301cran pour un message enregistre\u0301 lors de la premie\u0300re demi-finale du Concours Eurovision de la chanson 2025 a\u0300 Ba\u0302le, le 13 mai 2025 en Suisse (AFP\/Archives \u2013 SEBASTIEN BOZON)<\/p>\n<p>Comme de nombreuses pathologies neurologiques, aucun traitement n\u2019a fait ses preuves pour gue\u0301rir le syndrome de la personne raide. En revanche, il est crucial de proposer aux patients un suivi qui permette de limiter les sympto\u0302mes. S\u2019il n\u2019est pas traite\u0301, le syndrome finit en effet par avoir un impact significatif sur la capacite\u0301 d\u2019une personne a\u0300 effectuer des ta\u0302ches quotidiennes de routine.<\/p>\n<p>\u00ab De nombreux patients perdent leur capacite\u0301 a\u0300 marcher de manie\u0300re autonome et la raideur se ge\u0301ne\u0301ralise, entrai\u0302nant un de\u0301clin ge\u0301ne\u0301ral de l\u2019e\u0301tat fonctionnel et de la qualite\u0301 de vie \u00bb, souligne Orphanet. Il n\u2019existe actuellement pas de protocole unique chez les me\u0301decins pour faire face aux sympto\u0302mes, un consensus e\u0301tant difficile a\u0300 e\u0301tablir au vu de la rarete\u0301 des cas.<\/p>\n<p>\u00ab Plus to\u0302t c\u2019est diagnostique\u0301, mieux c\u2019est \u00bb<\/p>\n<p>Toutefois, l\u2019approche consiste ge\u0301ne\u0301ralement a\u0300 articuler certains me\u0301dicaments, en particulier des relaxants musculaires tels les benzodiaze\u0301pines, avec des approches non me\u0301dicamenteuses comme de l\u2019activite\u0301 physique. \u00ab Plus to\u0302t c\u2019est diagnostique\u0301, mieux c\u2019est \u00bb, souligne M. Pradat. \u00ab Apre\u0300s, il y a une variabilite\u0301 lie\u0301e aux caracte\u0301ristiques de la maladie, qui vont e\u0302tre diffe\u0301rentes d\u2019une personne a\u0300 l\u2019autre. \u00bb<\/p>\n<p>Dans le cas de Ce\u0301line Dion, sa me\u0301decin, le Pr. Piquet, a de\u0301taille\u0301 aupre\u0300s de plusieurs me\u0301dias un protocole qui me\u0302le me\u0301dicaments classiques, immunothe\u0301rapie, kine\u0301sithe\u0301rapie et re\u0301e\u0301ducation vocale. En fin de compte, la me\u0301diatisation de la chanteuse \u00ab a permis de mieux connai\u0302tre la maladie et que me\u0302me les me\u0301decins la connaissent mieux \u00bb, salue M. Pradat, se fe\u0301licitant \u00ab que les patients se sentent moins isole\u0301s dans ces maladies tre\u0300s rares \u00bb.<\/p>\n<p class=\"ap-article-footer-note\">Retrouvez plus d\u2019actualit\u00e9s et d\u2019analyses sur <span class=\"ap-highlight-country\">Senegal<\/span> sur le site <span class=\"ap-highlight-brand\">Africa Press<\/span><\/p>\n","protected":false},"excerpt":{"rendered":"<p>Africa-Press &#8211; Senegal. Depuis 2022, la chanteuse canadienne avait quasiment abandonne\u0301 la sce\u0300ne, a\u0300 l\u2019exception d\u2019une apparition lors de la ce\u0301re\u0301monie d\u2019ouverture des Jeux olympiques de Paris 2024. En cause, une maladie neurologique rare: le syndrome de la personne raide, e\u0301galement dit de Moersch-Woltman. La situation de la star internationale a attire\u0301 l\u2019attention sur cette [&hellip;]<\/p>\n","protected":false},"author":82,"featured_media":75774,"comment_status":"open","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"footnotes":""},"categories":[22,10],"tags":[44],"class_list":["post-75775","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-divers","category-toutes-les-actualites","tag-senegal-2"],"yoast_head":"<!-- This site is optimized with the Yoast SEO Premium plugin v26.1 (Yoast SEO v27.0) - https:\/\/yoast.com\/product\/yoast-seo-premium-wordpress\/ -->\n<title>C\u00e9line Dion et le syndrome de la personne raide - Senegal<\/title>\n<meta name=\"description\" content=\"-article-header-tag&quot;&gt; Africa-Press - Senegal. 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